Epidemiology


Etiology


Hypogonadotropic hypogonadism with hyposmia/anosmia

Pathophysiology


  • Defective migration of GnRH-releasing neurons from the olfactory bulbs to the hypothalamic preoptic nuclei → ↓ GnRH secretion and underdevelopment of the olfactory bulbs
  • ↓ GnRH → ↓ pituitary secretion of FSH and LH → ↓ testosterone in male individuals and ↓ estrogen in female individuals

Clinical features


  • Anosmia or hyposmia
  • Infertility

Diagnostics


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Treatment


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