Etiology


Pathophysiology

  • Auto-antibodies against collagen type IV in the renal and pulmonary capillary basement membrane
  • Possibly triggered by viral infections, lymphoma

Clinical features

  • Hemoptysis
  • Cough
  • Dyspnea
  • Nephritic syndrome
    • Usually presents as RPGN type 1
    • Proliferative glomerulonephritis

Diagnostics

  • Anti-GBM antibodies
  • Hemosiderin-filled macrophages in sputum
    • Due to intra-alveolar bleeding. Macrophages that subsequently phagocytose the erythrocytes are called “heart failure cells.”
    • These cells may also be detected in the sputum of patients with pulmonary infarction, vasculitis, or aspiration of blood.
  • Iron deficiency anemia

Treatment